Langerhans cell histiocytosis: a rare cause of cholestasis in adult patients. Case report. Histiocitosis de Langerhans: causa infrecuente de colestasis en el. a Unidad Médico-Quirúrgica de Enfermedades Respiratorias. Área de Neumopatías Intersticiales y Ocupacionales. Hospital Universitario Virgen del Rocío. Abstract. GOMEZ, ANA MARÍA et al. Langerhans cell histiocytosis in children. A description of 10 cases. CES Med. [online]. , vol, n.2, pp
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Manuscripts will be submitted electronically using the following web site: There are two patterns of involvement: The patient’s liver function gradually worsened and he was taken to a centre of reference for a liver transplant, he died before it could be performed.
However, if risk organs are involved, other chemotherapeutics are needed as well 6-mercaptopurine and metotrexate. Liver involvement in Langehan’s cell histiocytosis.
The magazine, referring to the Histoocitosis pediatric, indexed in major international databases: An ultrastructural study by transmission electron microscopy reveals the presence of Birbeck granules, although the most widely-used technique to reach a diagnosis is immunohistochemistry Langerhans cells are positive for staining with S, DC68 and CD1a. Vidal Serrano aE.
Si continua navegando, consideramos que acepta su uso. Liver transplantation in an adult with sclerosing cholangitis due to Langerhans cell histiocytosis. Archivos de Bronconeumologia http: If you are a member of the AEDV: Journal of Gastrointestinal and Liver Disease ; 15 1: In the diagnosis by immunohistochemistry identified Langerhans Cell Histiocytosis, the cases were classified as multisystemic -multifocal in 5 patients, unisystemic in 1 patients – unifocal histioctiosis in 1 patients -multifocal eosinophilic granuloma in 3 patients.
CiteScore measures average citations received per document published. This form of presentation is rare, and seems to be a variant of congenital self-healing reticulohistiocytosis.
Previous article Next article. A liver biopsy was performed after ruling out common pathologies.
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How hiatiocitosis cite this article. SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact. Two newborns with a solitary lesion on the groin and shoulder respectively of Langerhans cell histiocytosis LCH showing spontaneous resolution are reported. The Impact Factor measures the average number of citations received in a particular year by papers published in the journal during the two receding years.
The goal with the description of this cases series is to highlight the importance and awareness to a timely diagnosis and management of this entity, for a better quality of life and longer survival. It was decided to perform a bypass surgery and a hepaticojejunostomy and a gastrojejunostomy were performed.
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Eur Respir J, 9pp. All articles are subjected to a rigorous process of revision in pairs, and careful editing for literary and scientific style. Dear Editor, We present a 42 year old man, with langeerhans history of central diabetes insipidus since childhood, primary hyperthyroidism with negative antibodies and seizures since early adulthood.
SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact.
The disease prognosis and its response to treatment is better in the single system form, particularly with bone involvement, and much worse in the multi-system form, especially if several risk organs are involved liver, spleen, bone marrow and lung. We present a 42 year old man, with a history of central diabetes insipidus since childhood, primary histiocltosis with negative antibodies and seizures since early adulthood. April Pages Ihstiocitosis There are two patterns of involvement: Nevertheless, three langethans later the patient came to our hospital due to persistent analytical cholestasis and weight loss 30 kg since the initial episode of acute pancreatitisdespite an adequate intake of calories.
It is a monthly Journal that publishes a total of 12 issues, which contain these types of articles to different extents.
Histiocitosis de células de Langerhans en niños. Descripción de 10 casos
Clinical outcomes of pulmonary Langerhans’- cell histiocytosis in adults. Print Send to a friend Export reference Mendeley Statistics. Dina J, et al. Annals of Pediatrics is the Body of Scientific Expression of the Association and is the vehicle through which members communicate.